4-Methylumbelliferyl a-L-idopyranosiduronic acid sodium salt

4-Methylumbelliferyl alpha-L-idopyranosiduronic acid sodium salt is a carbohydrate acid and organic sodium salt applied as an indicator. It is the fluorogenic substrate used in assays of α-L-Iduronidase and iduronate-2-sulfatase for identifying Hurler syndrome, also called mucopolysaccharidosis type I (MPS I). The disorder is characterized by α -L iduronidase enzyme deficiency, resulting in the buildup of glucosaminoglycans. Tests measure the chemical products 4-MU-α-IdoA or fluorophate 4-MU emitted following the enzymatic action of 4-Methylumbelliferyl alpha-L-idopyranosiduronic acid sodium salt. The substance is a white crystalline powder and is soluble in ethanol, methanol and water.

Product Specifications
4-Methylumbelliferyl alpha-L-idopyranosiduronic acid sodium salt
4-Methylumbelliferyl a-L-iduronicacid sodium salt
Sodium 4-methyl-2-oxo-2H-chromen-7-yl α-L-idopyranosiduronate
Sodium(4-methylumbelliferyla-L-idopyranosid)urinate

Formula: C₁₆H₁₅NaO₉

MW: 374.27 g/mol

Storage/Handling: Store desiccated at -20°C.

PubChem Chemical ID: 71307170